Radical surgical treatment of neuroendocrine tumors
of the appendix in children – a Polish multicenter study

Małgorzata Panek; Marek Szymczak; Maria Stepaniuk; Wojciech Górecki; Aleksandra Gawłowska-Marciniak; Przemysław Wolak; Dariusz Zbyrad; Marek Rybkiewicz; Kamila Chrobak; Ryszard Noparlik; Jerzy Niedzielski; Przemysław Janik; Jan Nowak; Witold Miaśkiewicz; Andrzej Kamiński; Wojciech Fischer; Bożena Dembowska-Bagińska; Piotr Kaliciński

doi:10.5114/aoms/135706

4/2021 vol. 17

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PEDIATRICS / RESEARCH LETTER

Radical surgical treatment of neuroendocrine tumors of the appendix in children – a Polish multicenter study

Małgorzata Panek ¹

, Marek Szymczak ¹

, Maria Stepaniuk ², Wojciech Górecki ³

, Aleksandra Gawłowska-Marciniak ⁴, Przemysław Wolak ⁵, Dariusz Zbyrad ⁶, Marek Rybkiewicz ⁷, Kamila Chrobak ⁸, Ryszard Noparlik ⁹, Jerzy Niedzielski ¹⁰, Przemysław Janik ¹¹, Jan Nowak ¹², Witold Miaśkiewicz ¹³, Andrzej Kamiński ¹⁴, Wojciech Fischer ¹⁵, Bożena Dembowska-Bagińska ¹⁶, Piotr Kaliciński ¹⁷

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1	Department of Pediatric Surgery and Organ Transplantation, The Children’s Memorial Health Institute, Warsaw, Poland
2	Department of Pathology, The Children’s Memorial Health Institute, Warsaw, Poland
3	Department of Pediatric Surgery, Jagiellonian University Medical College, Krakow, Poland
4	Department of Pediatric Surgery and Oncology, Central Clinical Hospital Medical University of Lodz, Lodz, Poland
5	Department of Pediatric Surgery, Urology and Traumatology, Wladyslaw Buszkowski Children’s Hospital, Kielce, Poland
6	Department of Pediatric Surgery and Traumatology, Provincial Hospital, Tarnobrzeg, Poland
7	Department of Pediatric and Oncological Surgery, Urology and Hand Surgery, Pomeranian Medical University, Szczecin, Poland
8	Department of Children’s Developmental Defects Surgery and Traumatology, Medical University of Silesia in Katowice, Zabrze, Poland
9	Department of Pediatric Surgery, University Clinical Hospital, Opole, Poland
10	Department of Pediatric Surgery and Urology, Medical University of Lodz, Lodz, Poland
11	Department of Urology and Pediatric Surgery, The Ludwik Rydygier Provincial Polyclinic Hospital, Torun, Poland
12	Department of Pediatric Surgery and Urology, Karol Marcinkowski University Hospital, Zielona Gora, Poland
13	Department of Pediatric Surgery and Traumatology, ZZOZ, Ostrow Wielkopolski, Poland
14	Department of Pediatric Surgery and Urology, The Autonomous Public Children’s Clinic Hospital of the Medical University of Warsaw, Warsaw, Poland
15	Department of Pediatric Surgery, Hospital Municipal St. John Paul II, Elblag, Poland
16	Department of Pediatric Oncology, The Children’s Memorial Health Institute, Warsaw, Poland
17	Department of Pediatric Surgery and Organ Transplantation, The Children’s Memorial Health Institute, Warsaw, Poland

CORRESPONDING AUTHOR

Małgorzata Panek

The Children's Memorial Health Institute, Warsaw, Poland

Submission date: 2021-01-24

Final revision date: 2021-03-28

Acceptance date: 2021-04-11

Online publication date: 2021-04-23

Publication date: 2021-07-16

Arch Med Sci 2021;17(4):1128–1131

DOI: https://doi.org/10.5114/aoms/135706

KEYWORDS

TOPICS

ABSTRACT

Introduction:
The aim of the study was to examine management of pediatric appendiceal neuroendocrine tumors (ANETs) in Poland.

Material and methods:
Records of 27 patients with ANET diagnosed incidentally after appendectomy in the last decade.

Results:
Well-differentiated NET G1/G2 was diagnosed in 25 and well-differentiated neuroendocrine carcinoma G3 in 2 patients. Extended surgery was performed primarily in one instance and secondarily in 10 patients (right hemicolectomy in 9, ileocecal resection in 1) without adjuvant chemotherapy. Follow-up range was 1–121 months. Recurrence after secondary surgery was observed in 1 (3.7%) patient.

Conclusions:
Applying ENETS guidelines resulted in 100% overall survival of patients with NET.

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ISSN:	1734-1922